32 results
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
BEE Syndromes - ... affecting the brain ... Inflammatory causes ... optica spectrum disorder ... #inflammatory #differential
Leigh Syndrome 
History: 19-month-old girl with hypotonia, developmental 
delay, failure to thrive, and bilateral optic disc
Mitochondrial disorder ... elevation (can be ... #Clinical #MRI ... #Brain #Diagnosis ... #Radiology
CNS Ring-Enhancing Lesions - Immunocompromised vs Immunocompetent
Multiple Ring-Enhancing Lesions:
 • Toxoplasmosis (CD4 < 100)
 • Other
Diagnosis- Compatible syndrome ... + MRI lesions + ... #differential # ... diagnosis #causes ... #radiology #neurology
Imaging Patterns of Toxic and Metabolic Brain Disorders

Thalami, Mammillary Bodies and Tectum: Wernicke Encephalopathy
Dentate Nuclei: Metronidazole,
and Metabolic Brain ... : ODS #MRI #Patterns ... #Disorders #Clinical ... #Differential # ... Diagnosis #Radiology
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
Weakness - Differential ... Non-neuromuscular disorder ... nervous system: Brain ... dystrophies Work ... EMG) studies • MRI
Major neurocognitive disorders (MNCD): Diagnosis and workup 

1) Clinical diagnosis Cognitive impairment + loss of autonomy
2)
neurocognitive disorders ... 1) Clinical ... MRI, iADL scale, ... Aphaso-apraxo-agnosia syndrome ... MNCD #Dementia #Differential
BEE Syndromes - Non-inflammatory Causes

Immune-mediated conditions affecting the Brain, Eye, and Ear

Visual or auditory symptoms in
BEE Syndromes - ... affecting the Brain ... neuropathy (LHON) plus MRI ... lesions and clinical ... noninflammatory #differential
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Erythematosus (SLE) Clinical ... Demyelinating Syndrome ... , Seizure disorders ... autoantibodies that will cause ... thrombosis and/or blood-brain
Restrictive Cardiomyopathy - Diagnosis and Causes
Clinical: Dyspnea, Exercise Intolerance, ↑ "Right Sided-Symptoms" (ascites, hepatomegaly, ↑↑peripheral edema)
Physical
Diagnosis and Causes ... Clinical: Dyspnea ... Hyper-eosinophilc Syndrome ... Sarcomeric Protein Disorders ... #differential #
Causes of Secondary Hypertension - Workup and Differential Diagnosis
Approach (when evaluation should be done):
1. Severe or
Hypertension - Workup ... and Differential ... evaluation should be ... 109 mm Hg) with clinical ... #causes #Differential