62 results
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Clinical history ... concentration PET-CT ... IgG4 #Related #Disease ... #diagnosis #management
Lung Abscess - Diagnosis and Management Summary

Lung Abscess Etiology:
 • Necrosis of lung parenchyma by a
• Periodontal disease ... dentition/gingival disease ... Lung Abscess - Clinical ... loss • Late disease ... in early disease
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... Interstitial lung ... multifactorial mechanisms Hematologic ... Classification #Diagnosis ... #Differential #Causes
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
disease • ... Granulomatous disease ... • Liver diseases ... disease (GLILD) ... #diagnosis #management
Nontuberculous Mycobacteria (NTM) Infections 

Mycobacterial species other than those belonging to the Mycobacterium tuberculosis complex and
status NTM Cause ... disease ... Hematologic malignancy ... Lung Disease: ... Imaging, high res CT
Acute-on-Chronic Liver Failure (ACLF) Clinical Guidelines

ACLF = possibly reversible condition in those with CLD (± cirrhosis)
Failure (ACLF) Clinical ... underlying liver disease ... Brain Failure Lung ... Failure #Cirrhosis #Hepatology ... #diagnosis
Progressive Massive Fibrosis aka Complicated Silicosis.
Silicosis is a fibrotic lung disease caused by inhalation of crystalline
is a fibrotic lung ... disease caused ... With disease progression ... Calcification (seen in CT ... Fibrosis #Silicosis #clinical
Endocarditis Summary

Who?
Infectious:
• Pre-existing valvular disease
• Prosthetic valve
• Congenital heart disease
• IV substance use
• IV catheter
• Recent
Pre-existing valvular disease ... Congenital heart disease ... Rheumatic valvular disease ... • Metastatic disease ... #management #cardiology
Plain radiography of the abdomen revealed calcification of both adrenal glands. A homozygous mutation in LIPA
confirmed the diagnosis ... deficiency, or Wolman’s disease ... and gut, which causes ... calcifications #infant #NEJM ... #Wolmans #radiology
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis - Diagnosis ... , causes and management ... cryoglobulinemia vasculitis Clinical ... with refractory disease ... #Management