31 results
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... of Pulmonary Hypertension ... due to lung disease ... lung disease Other ... Classification #Diagnosis
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
Diagnostic algorithm ... testing; CTEPH, chronic ... dysplasia; CLD, chronic ... lung disease; LFT ... #Diagnosis #Peds
Causes of Pulmonary Hypertension - Differential Diagnosis Algorithm
Pulmonary Arterial Hypertension
 • Idiopathic
 • Associated with:
Causes of Pulmonary ... Differential Diagnosis ... Algorithm Pulmonary ... • Valvular Lung ... Metabolic Disorders Chronic
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
• Secondary to chronic ... lung disease (COPD ... • Hypoxia • Pulmonary ... hypertension ... MAT #Cardiology #Diagnosis
Right-Sided Heart Failure - Differential Diagnosis Algorithm
Cardiac Causes - Rule out Left-Sided Heart Failure (Most Common):
- Differential Diagnosis ... Diffuse Lung Disease ... Syndrome • Chronic ... Lung Infection ... Arterial Hypertension
Causes of Dyspnea - Differential Diagnosis Algorithm
Cardiac:
 • Dysrhythmia
 • Ischemia
 • Cardiomyopathy
 • Valvular disease
- Differential Diagnosis ... Bronchitis • Chronic ... • Interstitial lung ... hypertension ... #Differential #Diagnosis
Pulmonary Hypertension Groups - WHO Classification
Group I - Vascular remodeling of pulmonary arteries
 • Idiopathic, HIV,
Pulmonary Hypertension ... Group III - Chronic ... lung disease causing ... #Hypertension # ... Classification #diagnosis
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Clinical history ... head and neck, pancreas ... biliary, renal, lung ... concentration PET-CT
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) and Pulmonary Thromboendarterectomy
Chronic Thromboembolic Pulmonary Hypertension
Definition: mean pulmonary-artery pressure > 25mmHg
Chronic Thromboembolic ... Pulmonary Hypertension ... Plexiform-lesion formation Clinical ... Ventilation-perfusion lung ... have inoperable disease
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
, in advanced disease ... in the adjacent lung ... hypertension • ... of the affected lung ... high-resolution chest CT