17 results
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
due to lung disease ... lung disease Other ... pulmonary disease ... PHTN #Classification ... #Diagnosis #Differential
Causes of Pulmonary Hypertension - Differential Diagnosis Algorithm
Pulmonary Arterial Hypertension
 • Idiopathic
 • Associated with:
Causes of Pulmonary ... Differential Diagnosis ... Algorithm Pulmonary ... Metabolic Disorders Chronic ... PulmonaryHypertension #PHTN
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
Diagnostic algorithm ... testing; CTEPH, chronic ... dysplasia; CLD, chronic ... lung disease; LFT ... #Diagnosis #Peds
Pulmonary Hypertension Groups - WHO Classification
Group I - Vascular remodeling of pulmonary arteries
 • Idiopathic, HIV,
Pulmonary Hypertension ... lung disease causing ... #Hypertension # ... PHTN #Groups #WHO ... Classification #diagnosis
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
• Secondary to chronic ... lung disease (COPD ... • Hypoxia • Pulmonary ... hypertension ... MAT #Cardiology #Diagnosis
Right-Sided Heart Failure - Differential Diagnosis Algorithm
Cardiac Causes - Rule out Left-Sided Heart Failure (Most Common):
- Differential Diagnosis ... Diffuse Lung Disease ... Syndrome • Chronic ... Lung Infection ... Arterial Hypertension
Causes of Dyspnea - Differential Diagnosis Algorithm
Cardiac:
 • Dysrhythmia
 • Ischemia
 • Cardiomyopathy
 • Valvular disease
- Differential Diagnosis ... Bronchitis • Chronic ... • Interstitial lung ... hypertension ... #Differential #Diagnosis
Chronic Thromboembolic Pulmonary Hypertension (CTEPH) and Pulmonary Thromboendarterectomy
Chronic Thromboembolic Pulmonary Hypertension
Definition: mean pulmonary-artery pressure > 25mmHg
Pulmonary Hypertension ... Ventilation-perfusion lung ... have inoperable disease ... RebeccaSteinb17 #CTEPH #PHTN ... #Pulmonary #Hypertension
Portopulmonary Hypertension
Presence of pulmonary arterial hypertension in a patient with portal hypertension
No other obvious causes (chronic
Presence of pulmonary ... obvious causes (chronic ... lung disease, left ... heart disease, ... moderate (or worse) PPHTN
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
, in advanced disease ... in the adjacent lung ... hypertension • ... of the affected lung ... high-resolution chest CT