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Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
lung diseases ... LIP: lymphoid ... I-JIP: usual interstitial ... AIP: acute interstitial ... #Comparison #Table
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Interstitial Lung ... ILD caused by inhalation ... pneumonia (DIP) ... pneumonia (AIP) ... #differential #
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Causes of Interstitial ... Pneumonia • (UIP ... Pneumonia • (DIP ... Pneumonia • (LIP ... #ILD #Causes #Differential
Ground-glass opacity
Ground-glass opacity (GGO) represents:
- Filling of the alveolar spaces with pus, edema, hemorrhage, inflammation or
Thickening of the interstitium ... lung disease (i.e ... predominance: UIP ... , NSIP, DIP. - Centrilobular ... #GroundGlass #Differential
The idiopathic interstitial pneumonias (IIPs) comprise a heterogenous group of disorders. 
They represent fundamental responses of
indicates unknown cause ... findings of NSIP, UIP ... , OP and LIP have ... #Diagnosis #Radiology ... IdiopathicInterstitialPneumonia #ILD
Differential diagnosis on HRCT
Most of our knowledge about imaging findings in interstitial lung disease comes from
Differential diagnosis ... lung disease comes ... lung disease and ... UIP can be suspected ... #Diagnosis #Radiology
UIP
UIP is a histologic pattern of pulmonary fibrosis.
On a chest X-ray UIP manifests as a reticular
UIP UIP is a histologic ... a chest X-ray UIP ... can suspect UIP ... #CXR #UIP #Reticular ... #Interstitial #
On the left a chest film of a patient with UIP due to IPF.
The findings on
a patient with UIP ... preference also think 'UIP ... #CXR #CTChest # ... UIP #UsualInterstitialPneumonitis ... #Usual #Interstitial
The fourth pattern includes abnormalities that result in decreased lung attenuation or air-filled lesions.
These include:
- Emphysema
-
- Emphysema - Lung ... cysts (LAM, LIP ... #Diagnosis #Radiology ... LowAttenuation #Differential ... #Diagram #Comparison
The CXR demonstrates a reticular interstitial pattern with a preference at the lung bases.
The HRCT demonstrates
The CXR demonstrates ... preference at the lung ... bases. ... #Clinical #Radiology ... #CXR #UIP #CTChest