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Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... meningitis), MCC CNS symptoms ... Behcet disease) Differential ... inhibitors • Uveitis- Ophthalmology ... management #signs #symptoms
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
GI - Felty syndrome ... • Felty's syndrome ... Scleroderma Thickened skin ... , Marfan syndrome ... #joint #pain #differential
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
Conditions With Arteritis ... yrs - Cranial symptoms ... Polyarteritis nodosa: - Skin ... Ulceration GI tract - Ocular ... #Differential #
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
- Differential ... IgM deposits • Nodular ... : • Temporal arteritis ... • Takayasu's arteritis ... Disease • Cogan syndrome
Joint Disorders - Differential Diagnosis Algorithm
Monoarthritis
 • Septic
 • Crystalline
     - Gout
Joint Disorders - Differential ... - (Reiter’s syndrome ... - with the skin ... should have other symptoms ... Disorders #msk #Differential
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitides - Differential ... ulcers, cutaneous, ocular ... • Cogan Syndrome ... : - Ocular inflammatory ... Presentation - Systemic Symptoms
Leg Pain - Differential Diagnosis Framework

Bone/Joint Causes of Leg Pain:
 • Fracture
 • Arthritis
 • Gout/pseudogout
Leg Pain - Differential ... • Fracture • Arthritis ... • Arthritis ... thrombophlebitis Skin ... #Leg #pain #differential
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... Vasculitis Differential ... Presentation: Systemic Symptoms ... • Progressive symptoms ... : Ocular inflammatory
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Skin Conditions ... • Gonococcal arthritis ... Antiphospholipid-antibody syndrome ... • Psoriatic arthritis ... #rashes #differential
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Criteria for Behget's Syndrome ... vasculitis - Skin ... Wide variety of skin ... vasculitis) • Arthritis