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Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... Diagnosis Framework ... : - Ig A (HSP) ... Disease • Cogan syndrome ... #differential #diagnosis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... : • Behçet Syndrome ... • Cogan Syndrome ... Differential Diagnosis ... Cryoglobulins • HIV
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
- Purpura - Skin ... HBV infection, HIV ... reticularis & skin ... Labs/Diagnosis: ... Cryoglobulins #diagnosis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... Differential Diagnosis ... of shoulder and hip ... • Behcet syndrome ... • Cogan syndrome
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- Differential Diagnosis ... purple, hemorrhagic skin ... Kasabach-Merritt syndrome ... Gardner-Diamond syndrome ... #Differential #Diagnosis
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... response to local skin ... retinal damage) • Skin ... test (this is a skin ... #diagnosis #management
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Sjögrens (15%) Skin ... Butterfly rash, Vasculitis ... Aseptic necrosis of hip ... Demyelinating syndromes ... signs #symptoms #diagnosis
Orthopedic Emergencies
Compartment Syndrome
 • An increase in compartment pressure to the point where tissue perfusion is
Orthopedic Emergencies ... tibia/fibula) and hip ... • Diagnosis: ... over the involved skin ... area of erythema, skin
What is a Boxer’s fracture?? Fracture of the 4th or 5th metacarpal neck
 - Common in
Always check for skin ... – compartment syndrome ... Management: - ... Hand #Metacarpal #Diagnosis ... #Orthopedics
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
Lyme disease, Vasculitis ... Scleroderma Thickened skin ... Heberden's nodes (DIP ... Bouchard's nodes (PIP ... #differential #diagnosis