5 results
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation ... • Systemic lupus ... SJIA], systemic lupus ... with leukopenia, anemia ... #Rheumatology
Systemic Lupus Erythematosus - Diagnosis
Manifestations:
 - Arthritis 69%
 - Malar rash 40%
 - Fever 36%
 -
Arthritis 69% - Malar ... rash 40% - Fever ... - Hemolytic anemia ... sclerosis, Still's disease ... #differential #rheumatology
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
weight loss, and fever ... Photosensitivity • Malar ... lymphopenia, low PLT • Anemia ... to: Arthritis, Fever ... Chronic B-cell activation
Fever After International Travel

Infectious Disease:
• Endemic in either the destination or home region

Viral Syndromes:
Arboviral infections, a
shock syndrome may ... No hemolytic anemia ... Babesiosis • Plasmodium ... Most cases of malaria ... • Falciparum malaria
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
▪ Autoimmune diseases ... (often termed MAS-HLH ... - Cytopenias (anemia ... Fever b. ... Diagnosis #Management #Hematology