53 results
Aplastic Anemia and Bone Marrow Failure Syndromes with Pancytopenia

Fanconi Anemia
Acquired Aplastic Anemia
Dyskeratosis Congenita & Telemore Biology
Aplastic Anemia ... Marrow Failure Syndromes ... Anemia Acquired Aplastic ... Dyskeratosis Congenita ... anemia #diagnosis #Hematology
Aplastic Anemia - Overview

Who?
• M = F
• 3 peaks:	1) Childhood	2) 15-25 years	3) >60 years

What?
• Aplastic anemia
Constitutional Syndromes ... Constitutional Syndromes ... , Dyskeratosis congenita ... marrow-failure syndromes ... Anemia #oncology #hematology
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
HLH syndrome 5. ... FISH • Acquired Aplastic ... Hypoplastic MDS • Congenital ... marrow failure syndrome ... Diagnosis #Algorithm #Hematology
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
HLH syndrome 5 ... FISH • Acquired Aplastic ... Hypoplastic MDS • Congenital ... marrow failure syndrome ... Diagnosis #Algorithm #Hematology
Causes of Pediatric Wheezing - Differential Diagnosis Algorithm
CXR Abnormal:
 • Pulmonary Sequestration
 • Congenital Adenoid Cystic
Causes of Pediatric ... Sequestration • Congenital ... Vascular Compression Syndrome ... #Causes #Peds #Pediatrics
Causes of Depressed / Lethargic Newborn - Differential Diagnosis Algorithm
Maternal Related:
 • Drugs (Ex. SSRI)
 •
Hypertension Congenital ... Birth Injury • Congenital ... Infection • Congenital ... Respiratory Distress Syndrome ... #Causes #Peds #Pediatrics
Causes of Thrombocytopenia - Differential Diagnosis Algorithm
 
Decreased Megakaryopoiesis
 • Aplastic Anemia
 • Toxic Damage (e.g.
Megakaryopoiesis • Aplastic ... Non-lmmune: • HELLP Syndrome ... Algorithm #Causes #Hematology
Marcus-Gunn Jaw-Winking syndrome from congenital neurosyphilis

Sucking elicits blinking.  Once you see it you won't forget.

Dr.
Marcus-Gunn Jaw-Winking syndrome ... from congenital ... #Jaw #Winking #syndrome ... video #neurology #pediatrics
Causes of Pediatric Constipation - Differential Diagnosis Algorithm
Dietary / Functional:
 • Insufficient Volume / Bulk
Neurologic:
 •
Causes of Pediatric ... Lesions • Myotonia Congenita ... Guillain-Barré Syndrome ... #Causes #Peds #Pediatrics
Staphylococcal Scalded Skin Syndrome (SSSS) 
(aka Ritter disease)

#Staphylococcal #Scalded #Skin #Syndrome #SSSS #Diagnosis #Pediatrics #Dermatology #Ritter
Staphylococcal Scalded Skin Syndrome ... Scalded #Skin #Syndrome ... SSSS #Diagnosis #Pediatrics ... #Dermatology #Ritter