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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... #Vessel #Size #Classification ... #Differential #Algorithm
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... central nervous system ... disease - systemic ... lupus erythematosus ... dermatomyositis #Size #Classification
EULAR/ACR Classification Criteria for Systemic Lupus Erythematosus
Clinical Domains:
 • Constitutional domain: Fever
 • Cutaneous domain: Non-scarring
EULAR/ACR Classification ... Criteria for Systemic ... Renal domain: Proteinuria ... #EULARACR #Classification ... Criteria #SLE #Systemic
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
• Hematuria, proteinuria ... inflammation Others: • Lupus ... central nervous system ... lupus erythematosus ... #rheumatology #classification
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... Immune Complex: Systemic ... lupus erythematosus ... Rheumatoid arthritis, Systemic ... • Urinalysis (proteinuria
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
SLE (Systemic Lupus ... Skin Disease Classification ... ANCA-associated vasculitis ... (non-nephrotic proteinuria ... nephrotic-range proteinuria
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
activate the immune system ... • Vasculitis ... disorder (e.g. systemic ... lupus erythematosus ... diagnosis #types #classification
Causes of Pericarditis - Differential Diagnosis Algorithm
Viral:
 • Coxsackie
 • Echovirus
 • Adenovirus
 • Epstein-Barr virus
Differential Diagnosis Algorithm ... arthritis • Systemic ... lupus erythematosus ... spondyloarthropathies • Vasculitis ... Differential #Diagnosis #Algorithm
Lupus Nephritis - Diagnostic approach to kidney disease associated with systemic lupus erythematosus (SLE)
SLE patient develops
Lupus Nephritis ... associated with systemic ... develops new: • Proteinuria ... with evidence of proteinuria ... Nephritis #diagnosis #algorithm