76 results
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Clinical Classification ... due to lung disease ... lung disease Other ... pulmonary disease ... , Gaucher disease
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis Clinical ... remission - Refractory ... associated with refractory ... disease Dr.
AECOPD 
 Acute exacerbation of chronic obstructive pulmonary disease. 
COPD #clinical
chronic obstructive pulmonary ... disease. ... COPD #clinical
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... cancers • Systemic diseases ... autoinflammatory diseases ... hepatitis • Pulmonary
Posterior Reversible Encephalopathy Syndrome (PRES) - Diagnosis
Clinical Features:
 • Altered mental status (Either lethargy, confusion, or
PRES) - Diagnosis Clinical ... constant, global, and refractory ... • Autoimmune disease ... Risk Factor + Clinical
Sarcoidosis 
Non-caseating granulomas (Composed of T-helper & inflammatory cells) 
Clinical:
 • Disease fatal in 10% of
inflammatory cells) Clinical ... : • Disease fatal ... polyarthritis • Pulmonary ... Symptoms #Signs #Pulmonary
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
ANA ≠ Autoimmune Disease ... likely it will be clinically ... connective tissue disease ... • Rheumatic Diseases ... , Interstitial Pulmonary
Leptospirosis
Pathogen: Leptospira (interrogans, kirschneri, noguchii)
Risk Factors:
 • Occupational exposure - Farmers, ranchers, trappers, veterinarians
 • Recreational
Presentation: • Mild disease ... Meningitis • Weil's Disease ... failure • Severe pulmonary ... disease ARDS Diagnosis ... Epidemiologic exposure + clinical
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Syndrome Systemic disease ... association • M > F Clinical ... Inflammatory eye disease ... Behcet syndrome (Clinical ... azathioprine • Severe or refractory
Differential Diagnosis - Noninfectious Causes of Fever

CRITICAL DIAGNOSES:
 - Acute myocardial infarction
 - Pulmonary embolism or
Causes of Fever CRITICAL ... infarction - Pulmonary ... Transfusion reaction - Pulmonary ... - Sickle cell disease ... Sarcoidosis - Crohn disease