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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and often causes arthritis ... Vasculitis: + MPO-ANCA ... vesicular eruption - Joints ... and branches • GCA ... differential #diagnosis #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
ANCA Associated ... polyangiitis - EGPA - GPA ... : • Temporal arteritis ... • Takayasu's arteritis ... #skin #dermatology
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Associated with Joint ... Hypersensitivity vasculitis ... Sarcoidosis • GPA ... Antiphospholipid-antibody syndrome • Vasculitis ... #joint #pain #skin
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Elevated ESR and CRP GCA ... develop in pts with GCA ... vesicular eruption • Joints ... Palpable purpura, joint ... Differential #Diagnosis #Rheumatology
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
Associated with Joint ... Lyme disease, Vasculitis ... Scleroderma Thickened skin ... Heberden's nodes (DIP joints ... differential #diagnosis #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... surfaces of the joints ... • Giant cell arteritis ... #dermatology #rash ... #diagnosis #rheumatology
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
arteritis (GCA) ... systemic inflammatory vasculitis ... differential diagnosis = vasculitis ... Role of temporal ... required due to skip
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
3rd Decade Skin ... : • Joint pain ... arthropathy • 90% joints ... Seizures • Strokes Skin ... anti-Ro/SSA can rule
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
- Purpura - Skin ... reticularis & skin ... arthralgia, and arthritis ... DDX: • ANCA (Antineutrophil ... SLE), rheumatoid arthritis
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
inflammation of the joints ... and pain of the joints ... lymphoma, breast CA ... - Hematologic ... Leukocytoclastic vasculitis