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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... #Vessel #Size #Classification ... #Differential #Algorithm
Systemic Lupus Erythematosus: Gastrointestinal Manifestations
 - Thrombosis of vessels in the pancreas, Vasculitis -> Acute Pancreatitis
Systemic Lupus Erythematosus ... the pancreas, Vasculitis ... distension #Systemic ... Erythematosus #SLE ... Complications #pathophysiology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... Vasculitis Vasculitis ... central nervous system ... disease - systemic ... dermatomyositis #Size #Classification
Commonly Used Clinical Grading Systems
 • Edema Grading Scale
 • Hepatic Encephalopathy Grading (West Haven Criteria)
Clinical Grading Systems ... Edema Grading Scale ... Criteria) • Systolic ... • Grady Coma Scale ... #classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
central nervous system ... diseases, such as systemic ... Presentation - Systemic ... , and SLE) • Urinalysis ... #rheumatology #classification
Petechiae/Purpura - Diagnostic Algorithm. Pathophysiology: 1) Represent the passage of erythrocytes from the intravascular to extravascular
Purpura - Diagnostic Algorithm ... Pathophysiology: ... trauma, infection, vasculitis ... process such as vasculiitis ... Purpura #Palpable #Algorithm
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
antibodies) • Systemic ... ) • Systemic sclerosis ... scleroderma) - Anti-Scl ... ANCA-Associated Vasculitis ... Renal-limited vasculitis
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
activate the immune system ... diseases: - 10% SLE ... disorder (e.g. systemic ... erythematosus (SLE ... diagnosis #types #classification
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Clinical Features of Systemic ... Lupus (SLE) General ... Butterfly rash, Vasculitis ... joints Nervous system ... #systemic #erythematosus
Lupus Classification
Spontaneous Lupus
 - Cutaneous Lupus Erythematosus (CLE)
 - Systemic Lupus Erythematosus 
Drug-Induced Lupus
 - Drug-Induced
Lupus Classification ... ) - Systemic Lupus ... (SCLE-DIL) - ... Drug-Induced Systemic ... Lupusreference #Lupus #Classification