11 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
response to local skin ... injury) • Neurologic ... test (this is a skin ... disease) Differential ... diagnosis #management #signs
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... symptomatology Differential ... IgA-associated vasculitis, Behcet ... Renal #Syndrome #differential ... #diagnosis #nephrology
Sarcoidosis 
Non-caseating granulomas (Composed of T-helper & inflammatory cells) 
Clinical:
 • Disease fatal in 10% of
Clinical: • Disease ... exertion • Neurologic ... neuropathies • Skin ... Diagnosis #Symptoms #Signs ... #Pulmonary
CNS Ring-Enhancing Lesions - Immunocompromised vs Immunocompetent
Multiple Ring-Enhancing Lesions:
 • Toxoplasmosis (CD4 < 100)
 • Other
lymphoproliferative disease ... , may also see skin ... Sarcoidosis • Neuro Behcets ... Lesions #Brain #differential ... causes #radiology #neurology
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
Polyarteritis nodosa: - Skin ... sinusitis - pulmonary ... Leukocytoclastic vasculitis Behcet's ... disease: - Oral ... Coronaries #Arteritis #Differential
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... purpura: Strong sign ... , neurologic, and ... cognitive impairment, neurologic ... vasculitis • Behcet
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitides - Differential ... progressing GN • New pulmonary ... VASCULITIS: • Behçet ... Differential ... purpura: strong sign
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
Pulmonary ... Spondyloarthropathies, SLE • Pulmonary ... syndrome - SLE Neurologic ... Scleroderma Thickened skin ... #joint #pain #differential
Spinal Cord Disorders - Differential Diagnosis Framework

Spinal cord neurological lesion:
Clinical findings:
 • Symptoms and signs below
Cord Disorders - Differential ... • Symptoms and signs ... - Sarcoidosis, Behcet ... disease - SLE ... disorders #diagnosis #neurology
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
super-antigen mediated disease ... • Bilateral signs ... disease - Sjogren ... diagnosis #management #neurology ... #differential