13 results
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... < 5% of mixed cryoglobulinemia ... TerrierBen #NonHCV #Cryoglobulinemia ... #Vasculitis #Rheumatology ... #Mixed #Cryoglobulinemic
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... • Absence of skin ... neuropathy • Type II cryoglobulinemia ... #Involvement #Cryoglobulinemia ... Cryoglobulinemic
Cryoglobulinemia Vasculitis
#rheumatology #diagnosis #signs
Cryoglobulinemia ... Vasculitis #rheumatology ... #diagnosis #signs
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Cryoglobulinemia ... , in Mixed Cryoglobulinemia ... Triad - Mixed Cryoglobulinemia ... - 10% SLE or RA ... classification #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... Secondary: CTD: SLE, RA ... Skin Findings: ... Urticarial/LCV) - Cryoglobulinemic ... #rheumatology #
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
ANCA +MPO) • Cryoglobulinemic ... Vasculitis - Skin ... purpura: strong sign ... Low levels mixed cryoglobulinemia ... differential #diagnosis #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... purpura • Mixed cryoglobulinemia ... Granulomatous vasculitis ... • Necrotising vasculitis ... rash #diagnosis #rheumatology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
purple, hemorrhagic skin ... • Ig A vasculitis ... /HSP • Cryoglobulinemia ... Differential #Diagnosis #hematology ... #rheumatology #
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Alpha & Mu) Skin ... Immunotactoid GN & Cryoglobulinemic ... thrombosis+Pulm HTN+skin ... Autoimmunity: • -MM/WM: Vasculitis ... (Cryoglobulinemic
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... , sepsis or cryoglobulinemia ... Calciphylaxis • Cryoglobulinemia ... Warfarin-induced skin ... Cryofibrinogenemia #diagnosis #rheumatology