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2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Polyangiitis (GPA) and ... Microscopic Polyangiitis ... Polyangiitis #GPA #Microscopic ... ACR2021 #Management #rheumatology ... #algorithm #vasculitis
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... retroorbital mass) • Microscopic ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis ... #vasculitis #differential
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
Vasculitis A group ... , small-vessel vasculitis ... polyangiitis (GPA), microscopic ... involvement - PR3>MPO Microscopic ... PR3 #Diagnosis #Rheumatology
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
, and small vessel ... an important concept ... can affect any ... medium arteries and ... #Diagnosis #Rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Microscopic Polyangiitis ... (MPA) - ANCA Vasculitis ... Polyangiitis #GPA #Microscopic ... #Vasculitis #Management ... Guidelines #algorithm #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... • ANCA Associated ... : - Microscopic ... #dermatology #rheumatology
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... inflammation: • Microscopic ... #Vasculitis #differential ... diagnosis #algorithm #rheumatology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Vasculitis of ... small vessels - ANCA-associated ... granulomatosis - microscopic ... drugs, malignomas, and ... Vessels #Diagnosis #Rheumatology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (GPA), Microscopic ... @MithuRheum #Vasculitis ... Guidelines #algorithm #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... ): • Microscopic ... LFT • ESR • ANA ... Dx: GPA, EGPA, microscopic ... differential #diagnosis #rheumatology