43 results
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Behcet's Syndrome ... manifestations can ... refractory lesions Ocular ... #Treatment #management ... #pharmacology #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Secondary: CTD ... IgM deposits • Nodular ... Disease • Cogan syndrome ... Vasculitis #skin #dermatology ... #rheumatology #
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... prick test that can ... Leukemia, Lymphoma Ocular ... #diagnosis #management ... signs #symptoms #rheumatology
2019 EULAR recommendations for thrombosis in (Antiphospholipid Syndrome) APS
Venous Thrombosis - Arterial Thrombosis
INR Target
Duration
Recurrence

Dr. Laurent ARNAUD
2019 EULAR recommendations ... Antiphospholipid Syndrome ... Antiphospholipid #Syndrome ... #APS #management ... #hematology #treatment
Anterior Non-necrotizing Scleritis - Slit Lamp Ocular Examination

This 57 yo WM reported to clinic complaining of
Scleritis - Slit Lamp Ocular ... reported no pain and had ... This patient had ... ophthalmology #physicalexam ... #rheumatology #
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Entities That Can ... capillary leak syndrome ... Hypergammaglobulinemic macular ... Autoantibodies: • WAIHA • CAD ... Paraproteinemias #Hematology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
sites such as the collar ... TNF blockers had ... #Rheumatology # ... diagnosis #management ... #Dermatology
Oroya Fever
Hematologic disease caused by Bartonella bacilliformis
Restricted to the Andes highlands of Peru & Ecuador
B. bacilliformis:
Oroya Fever Hematologic ... : AMS (carries bad ... : ​• Miliar → Nodular ... → Mular DIAGNOSIS ... Fever #diagnosis #management
Consensus Indications for Irradiated RBC Transfusions:

Cellular blood components are irradiated for the prevention of TA-GVHD. Transfused
T lymphocytes can ... disorders (DiGeorge Syndrome ... #Indications #Hematology ... #BloodBank #Management
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
proteins which can ... Cryofibrinogenemia Can ... pulmonary emboli, and ocular ... Antiphospholipid syndrome ... #hematology