14 results
Approach to the Hypercoagulable State
Arterial thromboembolism
→ Cardiac rhythm monitoring, Echocardiogram, Vascular imaging
→ Test for APS, particularly
Hypercoagulable State Arterial ... rhythm monitoring, Echocardiogram ... risk actor for arterial ... Hypercoagulable #Workup #hematology ... diagnosis #algorithm #hematology
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
Distribution of vessel involvement ... with respect to arterial ... involvement, and ... #Diagnosis #Rheumatology
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
internal organ involvement ... PAH (pulmonary arterial ... Musculoskeletal: joint involvement ... Scleroderma #SSc #rheumatology
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
pulmonary and renal involvement ... evaluate pulmonary involvement ... o infection • Echocardiogram ... blood retum in serial
Disseminated Intravascular Coagulation (DIC) Overview

Increased Clotting and Consumption of Clotting Factors

Findings:
 • Bleeding
 • Recent history
Thromboembolism (7%) • CNS involvement ... variants of both • Acral ... treatment #management #hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Vascular Disease: Arterial ... ulcers • Eye involvement ... signs #symptoms #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
nervous system involvement ... Thrombosis and arterial ... Urinalysis (Renal involvement ... differential #diagnosis #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Bone and joint involvement ... , parts of the axial ... SAPHO #Syndrome #Rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
purpura, joint & gut involvement ... nervous system involvement ... Thrombosis and arterial ... Differential #Diagnosis #Rheumatology
Amyloidosis on POCUS Echocardiogram - Parasternal long axis (PLAX)
Pt with systemic AL amyloidosis presents with 1
Amyloidosis on POCUS Echocardiogram ... thickening and biatrial ... amyloidosis with cardiac involvement ... POCUS #clinical #Echocardiogram