14 results
Management of adult IgA Vasculitis (Henoch-Schönlein purpura) - Treatment algorithm for the management of IgAV patients
Henoch-Schönlein purpura) - Treatment ... according to organ involvement ... outcome of renal involvement ... Treatment remains ... HSP #Management #Treatment
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis ... manifestations - Skin involvement ... purpura - Renal involvement ... - Joint involvement ... neuropathy Treatment
Retinal Vasculitis in Takayasu’s Arteritis- ...Ophthalmologic examination revealed severe impairment, with perception of only light in
Retinal Vasculitis ... , large-vessel vasculitis ... associated with involvement ... and initiated treatment ... angiography #retinal #vasculitis
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
nervous system (CNS) involvement ... diagnosis and treatment ... ANCA-associated vasculitides
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
years, multiorgan involvement ... with response to treatment ... No necrosis, No vasculitis ... IgG4+ cells" Treatment ... phenotypes #workup #treatment
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... pulmonary and renal involvement ... palpable purpura 2/2 vasculitis ... evaluate pulmonary involvement ... diagnosis #management #treatment
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... panuveitis, retinal vasculitis ... MCC-small vessel vasculitis ... ulcers • Eye involvement ... Arthritis, AS Treatment
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Multi-System Involvement ... Autoimmunity: • -MM/WM: Vasculitis ... Hypergammaglobulinemic macular Vasculitis ... Differential #Diagnosis #Oncology
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
extra cutaneous involvement ... Leukocytoclastic vasculitis ... Treatment: - Systemic ... #dermatology #oncology
Lyme Disease - Diagnosis and Management Summary

Lyme Disease Epidemiology:
- Spirochete
- Reservoir: small mammals & birds
- Transmitted
Iridocyclitis - Retinal vasculitis ... Lyme Disease Treatment ... days for Neuro involvement ... Diagnosis #Management #treatment