43 results
Approach to Von Willebrand disease (VWD)

By Matthew Ho, MD PhD @MatthewHoMD

#VWD #Von #Willebrand #VonWillebrand #disease #hematology
Willebrand disease (VWD ... MatthewHoMD #VWD ... VonWillebrand #disease #hematology ... #algorithm #diagnosis
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... of GP Ib/IX/V [vWF ... Thrombasthenia • Defect ... α-granules (contains vWF ... differential #diagnosis #hematology
Platelet disorders and Aggregometry
Glanzmann Thrombasthenia
 • Defective aggregation to all agonists except ristocetin
 • Normal platelet,
also be seen in vWD ... differentiate vWD ... BS by measuring vWF ... with qualitative defects ... Platelet #disorders #hematology
Pathophysiology of Hemolytic Anemia
 - Defects in RBC internal contents (thalassemia, hemoglobinopathies, and metabolic defects)
 -
Pathophysiology ... and metabolic defects ... ) - Defects in ... environment #Pathophysiology ... Hemolytic #Anemia #hematology
Cardiac Murmurs and Maneuvers

An algorithm demonstrating the effect of various maneuvers on systolic murmurs. 
TR, tricuspid
Maneuvers An algorithm ... demonstrating the effect ... aortic stenosis; VSD ... ventricular septal defect ... The effect of squatting
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
Differential Diagnosis Algorithm ... Non malignant hematologic ... ITP • Rebound effect ... Differential #Diagnosis #Algorithm ... #Causes #Hematology
Bleeding and Bruising - Differential Diagnosis Algorithm
 • Vascular System Defect - Congenital vs Acquired
 •
Differential Diagnosis Algorithm ... Vascular System Defect ... Acquired • Platelet Defect ... Differential #Diagnosis #Algorithm ... #pathophysiology
Polycythemia (Erythrocytosis) - Pathophysiology

#Polycythemia #Erythrocytosis #Pathophysiology #hematology #algorithm #differential #diagnosis
Erythrocytosis) - Pathophysiology ... Erythrocytosis #Pathophysiology ... #hematology #algorithm
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Thrombocytopenia • Platelet defects ... PURPURA: Platelet Defects ... syndrome Coagulation Defects ... Willebrand disease (VWD ... Differential #Diagnosis #hematology
Hemolytic Anemias - Differential Diagnosis Algorithm

Signs of anemia and hemolysis:
 • ↓ Haptoglobin
 • ↑ LDH
Differential Diagnosis Algorithm ... Extrinsic RBC Defects ... : Membrane defects ... Differential #Diagnosis #Algorithm ... #hematology