8 results
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated ... polyangiitis (GPA ... - C-ANCA pattern ... Anti-GBM disease ... #CANCA #PANCA #
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA ... ) - ANCA Vasculitis ... #ANCA #Vasculitis ... #Management #Treatment ... #ACR2021 #Guidelines
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
involvement: Anti-GBM Disease ... Negative IF): • PR3 ... -ANCA (C-ANCA): ... • MPO-ANCA (P-ANCA ... Glomerulonephritis #Vasculitis
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
) - ANCA Vasculitis ... alone in select pts ... #Polyangiitis #ANCA ... #Vasculitis #Management ... #Treatment #ACR2021
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: ANCA Associated ... - ANCA specific ... Granulomas - ANCA ... Vasculitis: + MPO-ANCA ... (Dx: GPA, EGPA,
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Summary Autoimmune ANCA ... vasculitis (AAV ... Auto-antibodies: ANCA ... differential #diagnosis #management ... #treatment
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
: ANCA Associated ... Pauci Immune (ANCA ... -ANCA)): Microscopic ... No Granulomas (ANCA ... (-Granulomas) ANCA
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
Sjögren’s syndrome, ANCA-associated ... vasculitis - Infectious ... Hypoalbuminemia Treatment ... TAFRO #diagnosis #management ... #rheumatology #