7 results
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
tract, and often causes ... - GI tract: abdominal ... < 30 years - Aorta ... branches • GCA: - Aorta ... Supply gut -> abdominal
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... palpable purpura 2/2 vasculitis ... mononeuritis multiplex WORKUP ... Other tests: • CT ... #management #treatment
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
Retroperitoneum and aorta ... concentration PET-CT ... conventional imaging (aorta ... No necrosis, No vasculitis ... management #phenotypes #workup
Acute Kidney Injury - AKI Workup Algorithm and Differential Diagnosis
Baseline Investigations: full blood count with differential,
Kidney Injury - AKI Workup ... and Differential Diagnosis ... Glomerulonephritis / Vasculits ... : ANCA, ANA, Anti-GBM ... renal biopsy • Abdominal
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... < 30 years • Aorta ... Arteritis): • Aorta ... tract, and often causes ... gut involvement, abdominal
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
systemic inflammatory vasculitis ... those coming off aorta ... = vasculitis vs ... (Cornelia NEJM ... Treatment of GCA
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
kidney disease caused ... Workup: • Kidney ... clone detection • CT ... formation causing vasculitis ... microangiopathy Treatment