14 results
2019 EULAR recommendations for thrombosis in (Antiphospholipid Syndrome) APS
Venous Thrombosis - Arterial Thrombosis
INR Target
Duration
Recurrence

Dr. Laurent ARNAUD
2019 EULAR recommendations ... Antiphospholipid Syndrome ... ) APS Venous Thrombosis ... #APS #management ... #hematology #treatment
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Cutaneous Manifestations ... Systemic amyloidosis, Nodular ... , Syndrome Schnitzler ... monoclonal #gammopathy #Cutaneous ... manifestations #dermatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Primary: 50% Cutaneous ... IgM deposits • Nodular ... Disease • Cogan syndrome ... Vasculitis #skin #dermatology ... #rheumatology #
2019 EULAR Recommendations - Obstetrics Management in (Antiphospholipid Syndrome) APS
Previous Thrombosis?
Previous Pregnancy Complications?

Dr. Laurent ARNAUD @Lupusreference

#obstetrics
2019 EULAR Recommendations ... - Obstetrics Management ... ) APS Previous ... #APS #management ... EULAR2019 #guidelines #rheumatology
Leukostasis vs Tumor Lysis Syndrome
Leukostasis:
 • Pathophysiology: Large, immature blasts and high WBC count cause hyperviscosity
vs Tumor Lysis Syndrome ... : - Neuro: AMS ... have fever - ACS ... TLS #diagnosis #management ... #hematology
Differentiation Syndrome in APML
Epidemiology:
 • Incidence: common in APL (2-48% depending on the study)
 • Triggers:
Differentiation Syndrome ... Incidence: common in APL ... Differentiation #Syndrome ... APML #diagnosis #management ... #hematology #oncology
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
DERMATOMYOSITIS Cutaneous ... the face, or the anterior ... • Anti-TIF1y Abs ... with anti-NXP2 Abs ... #dermatology #diagnosis
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... vasculitis) • Cutaneous ... Reactive Arthritis, AS ... #diagnosis #management ... signs #symptoms #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
involvement: May involve anterior ... the collar bone ... #Rheumatology # ... diagnosis #management ... #Dermatology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
gangrenosum • Cutaneous ... capillary leak syndrome ... Hyperviscosity syndrome ... Hypergammaglobulinemic macular ... Paraproteinemias #Hematology