7 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Idiopathic • Normal ... Complement: IgA ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm ... #rheumatology
Complement Deficiency Testing Algorithm
 • Normal CH50 and AH50 AND High suspicion for complement deficiency
 •
Complement Deficiency ... Testing Algorithm ... suspicion for complement ... #Deficiency #Testing ... #Algorithm #hematology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
pulmonary disease, and ocular ... ulcers, cutaneous, ocular ... Syndrome: - Ocular ... against MPO • Complement ... #classification
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
period AND • Meeting ... Uveitis or retinal vasculitis ... Behcet's - Abnormal ... uveitis, retinal vasculitis ... Diagnosis #criteria #rheumatology
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
anti-Smith Ab, low complements ... Skin Disease Classification ... Erythematous, macular ... vein thrombosis Hematologic ... RNP antibodies, Complement
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
meet criteria for hematologic ... kidney function • Abnormal ... guide subtype classification ... tubulopathy) - Complement ... formation causing vasculitis
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
aortitis, mimics vasculitis ... - ↑ IgE, ↓ complement ... • Classification ... : 2019 ACR/EULAR ... Diagnosis #Management #Rheumatology