25 results
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
: Overwhelming clinical ... : HLH signs and ... symptoms can mimic ... #management #treatment ... #hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
accumulation of clinical ... Assessment • Clinical ... Cellular immune deficiency ... #management #treatment ... #summary #rheumatology
Cardiac Amyloid - Diagnosis, Signs, Symptoms and Management

Clinical Presentation
- exertional dyspnea
- peripheral edema
- exertional syncope
- peripheral
, Signs, Symptoms ... and Management ... Clinical Presentation ... #Signs #Symptoms ... #Cardiology #Staging
Iron Deficiency in Heart Failure - Diagnosis and Treatment Algorithm
Diagnosis: Ferritin <100 ng/mL (absolute ID) OR
Heart Failure - Diagnosis ... Ferritin <100 ng/mL ... order to alleviate symptoms ... #management #algorithm ... #cardiology #treatment
Aortic Stenosis - Diagnosis and Stages

Clinical Presentation
- Exertional dyspnea
- Chest pain
- Palpitations
- HF Symptoms (orthopnea, PND,
Aortic Stenosis - Diagnosis ... and Stages Clinical ... #Stages #Management ... #Signs #Symptoms ... #Cardiology
Iron Deficiency in Heart Failure
Pathophysiology:
Chronic heart failure leads to an increase in inflammatory cytokines → Inflammation
Iron Deficiency ... and iron release Diagnosis ... improvement in symptoms ... #heartfailure #diagnosis ... #management #cardiology
Post-Transplantation Lymphoproliferative Disorders (PTLD)
Definition: Lymphoid and/or plasmacytic proliferations that occur as a result of immunosuppression in
haploidentical>unrelated>HLA ... Conditioning regimen Signs ... , unexplained hematologic ... EBV viral load, signs ... #management #transplant
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
fever syndromes Clinical ... Fever is the main clinical ... 5000 to 10,000 ng/mL ... Activation #Syndrome #Diagnosis ... #Management #Hematology
Bullous Pemphigoid - Diagnosis and Management Summary
Pathophysiology: Autoantibody-mediated damage to epithelial basement membrane -> separation of
Bullous Pemphigoid - Diagnosis ... epidermis from dermis Clinical ... Signs/Symptoms/ ... Bullous #Pemphigoid #Diagnosis ... #Management #dermatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
common in Asia • HLA-B51 ... association • M > F Clinical ... CNS symptoms (headache ... #management #signs ... #symptoms #rheumatology