15 results
Inflammatory Myopathies
Dermatomyositis
 • Onset: Subacute
 • Pattern: Proximal
 • CK: Up to 50X ULN
 • Autoantibodies:
Inflammatory Myopathies ... of exclusion Necrotizing ... Autoimmune Myositis ... discontinued Inclusion ... #comparison #rheumatology
Idiopathic Inflammatory Myopathies (IIM's)

RASH + MUSCLE WEAKNESS → Consider idiopathic inflammatory myopathies (IIM's)

 • Overlap Myositis
Idiopathic Inflammatory Myopathies ... features of another autoimmune ... antisynthetase syndrome • Inclusion ... #IIMs #diagnosis ... #rheumatology #
Myositis and Myopathies
Polymyositis 
 • Progressive, symmetric muscle weakness 
 • Elevated CK, +Anti-Jo, +Anti-Mi2
Dermatomyositis
Myositis and Myopathies ... temporal arteritis Inclusion ... BostonChiefs #Myositis #Myopathies ... #differential #diagnosis ... #comparison #rheumatology
Myositis Specific Antibodies (MSAs)

Dermatomyositis: MDA5, TIF1y, NXP2, Mi-2, SAE
Anti-Synthetase Syndrome: Jo-1, PL7, PL12, EJ, OJ
Immune Mediated
): HMGCR, SRP Inclusion ... Antibodies #MSAs #clinical ... #diagnosis #rheumatology
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... not related to clinical ... l) : Vascular occlusion ... Cryoglobulinemia #Vasculitis #Diagnosis ... #Rheumatology #
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
associated with autoimmune ... and/or venous occlusions ... tissue • Angio: Occlusion ... #rheumatology # ... hematology
Susac Syndrome - Clinical Triad
 - Central nervous system dysfunction
 - Branch retinal artery occlusion
 -
Susac Syndrome - Clinical ... retinal artery occlusion ... SusacSyndrome #Triad #Diagnosis ... #Management #Rheumatology
Creatine Kinase - Causes of Elevated CK Levels
Acute CK Elevation (Pain > Weakness):
 • RHABDOMYOLYSIS
immobility • Critical ... - Metabolic Myopathies ... myopathy - Autoimmune ... PROXIMAL AND DISTA: Inclusion ... #differential #diagnosis
Autoimmune Hepatitis

Clinical Presentation
 - Highly variable clinical presentation, from subclinical disease to acute liver failure.
 -
Autoimmune Hepatitis ... , AIH diagnosis ... Histologic Findings - Exclusion ... BryanCUlrich #Autoimmune ... #Management #Hepatology
Diplopia - Double Vision - Differential Diagnosis Algorithm
Clinical Pearls:
 • Diplopia is almost always binocular.
 •
- Differential Diagnosis ... Algorithm Clinical ... of exclusion. ... Cataract/Lens Dislocation ... #Algorithm #Causes