1384 results
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... destructive sinusitis, pulmonary ... lung disease • Eosinophilic ... polyangiitis - Asthma. eosinophilia ... Cryoglobulinemic vasculitis
More common & convincing pneumonia mimics 

Aspiration pneumonitis, 
Pulmonary vasculitis, 
Acute eosinophilic pneummia,  
Cryptogeric organizing
pneumonitis, Pulmonary ... vasculitis, Acute ... eosinophilic pneummia ... of idiopathic pulmonary ... fibrosis (IPF), Pulmonary
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... ANCA-positive vasculitis ... (Eosinophilic granulomatosis ... ANCA-negative vasculitis ... IgA-associated vasculitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... • EGPA: - Eosinophilia ... arthritis, obstructive pulmonary
Non-Resolving Pneumonias: Etiologies
Unusual Infections:
 - Immunocompromised patients (e.g.: Mycobacterium, Aspergillosis, Nocardia)
 - Endemic Fungi (e.g.: Histoplasmosis,
disorders: - Vasculitis ... - Eosinophilic ... Others: - Pulmonary ... abnormalities (Pulmonary ... Pneumonia #diagnosis #pulmonary
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
• Idiopathic pulmonary ... Sarcoidosis • Vasculitis ... polyangiitis, Eosinophilic ... syndrome) • Eosinophilic ... #differential #pulmonary
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
progressing GN • New pulmonary ... MPO > PR3) • Pulmonary ... progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia ... Granulomas, IgE, pulmonary
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal ... Autoimmune ANCA vasculitis ... polyangiitis), EGPA (eosinophilic ... palpable purpura 2/2 vasculitis ... differential (check eosinophil
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... No Asthma and Eosinophilia ... Both asthma and eosinophilia ... and/or 10%) - Eosinophilic ... StanfordChiefs #ANCA #Vasculitis
Eosinophilic Pneumonia
When to suspect Eosinophilic Pneumonia? Non-resolving pneumonia + BAL > 25% eosinophils + excluded more
Eosinophilic Pneumonia ... When to suspect Eosinophilic ... diagnoses Acute Eosinophilic ... Consolidations AKA "inverse pulmonary ... Pneumonia #diagnosis #pulmonary