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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... • EGPA: - Eosinophilia ... arthritis, obstructive pulmonary ... purpura: strong sign
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
progressing GN • New pulmonary ... purpura: Strong sign ... MPO > PR3) • Pulmonary ... progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... destructive sinusitis, pulmonary ... lung disease • Eosinophilic ... polyangiitis - Asthma. eosinophilia ... Cryoglobulinemic vasculitis
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... No Asthma and Eosinophilia ... Both asthma and eosinophilia ... and/or 10%) - Eosinophilic ... StanfordChiefs #ANCA #Vasculitis
Eosinophilic Pneumonia
When to suspect Eosinophilic Pneumonia? Non-resolving pneumonia + BAL > 25% eosinophils + excluded more
Eosinophilic Pneumonia ... When to suspect Eosinophilic ... diagnoses Acute Eosinophilic ... Consolidations AKA "inverse pulmonary ... Pneumonia #diagnosis #pulmonary
Differential Diagnosis of Pulmonary Eosinophilia
Infection:
 • Helminthic: Loffler syndrome (Ascaris, hookworm, Strongyloides), Tropical pulmonary eosinophilia (lymphatic
Differential Diagnosis of Pulmonary ... Eosinophilia Infection ... Strongyloides), Tropical pulmonary ... Acute chronic pulmonary ... #Pulmonary #Differential
More common & convincing pneumonia mimics 

Aspiration pneumonitis, 
Pulmonary vasculitis, 
Acute eosinophilic pneummia,  
Cryptogeric organizing
pneumonitis, Pulmonary ... vasculitis, Acute ... eosinophilic pneummia ... of idiopathic pulmonary ... fibrosis (IPF), Pulmonary
Causes of Eosinophilia - Differential Diagnosis
Bugs:
 - Fungus (aspergillosis)
 - Viral (HIV)
 - Ectoparasites (scabies, myiasis)
Causes of Eosinophilia ... DRESS - AIN - Eosinophilic ... Asthma Tugs (vasculitis ... Syndrome - Chronic Eosinophilic ... coyefish379 #Eosinophilia
Eosinophil Disorders Testing Algorithm
INDICATIONS FOR TESTING:
 • Peripheral blood eosinophilia/hypereosinophilia uncovered incidentally during medical evaluation or
Eosinophil Disorders ... Peripheral blood eosinophilia ... specific symptoms • Eosinophilia ... secondary causes of eosinophilia ... organ-specific signs
ANCA Vasculitis - GPA, MPA, Eosinophilic GPA

doi:10.1038/s41572-020-0204-y

#ANCA #Vasculitis #GPA #MPA #Eosinophilic #rheumatology #diagnosis #comparison #table
ANCA Vasculitis ... - GPA, MPA, Eosinophilic ... 0204-y #ANCA #Vasculitis ... #GPA #MPA #Eosinophilic