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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... When to Consider Vasculitis ... • EGPA: - Eosinophilia ... tract, and often causes ... Presentation - Systemic Symptoms
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... • Progressive symptoms ... progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia ... tract, and often causes
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... polyangiitis), EGPA (eosinophilic ... differential (check eosinophil ... or serologies + symptoms ... Goodpasture's cause
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... No Asthma and Eosinophilia ... Both asthma and eosinophilia ... and/or 10%) - Eosinophilic ... StanfordChiefs #ANCA #Vasculitis
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... lung disease • Eosinophilic ... polyangiitis - Asthma. eosinophilia ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis
Eosinophilic Esophagitis (EoE) - Spectrum of Response
Non-response:
 • Histology: Persistent eosinophilia, ≥ 15 eos/hpf
 • Symptoms:
Eosinophilic Esophagitis ... Histology: Persistent eosinophilia ... : Persistent symptoms ... Histology: Reduced eosinophilia ... score < 2 #Eosinophilic
Eosinophil Disorders Testing Algorithm
INDICATIONS FOR TESTING:
 • Peripheral blood eosinophilia/hypereosinophilia uncovered incidentally during medical evaluation or
Eosinophil Disorders ... workup for specific symptoms ... for secondary causes ... (common causes ... organ-specific signs or symptoms
Eosinophilic Pneumonia
When to suspect Eosinophilic Pneumonia? Non-resolving pneumonia + BAL > 25% eosinophils + excluded more
Eosinophilic Pneumonia ... When to suspect Eosinophilic ... pneumonia + BAL > 25% eosinophils ... diagnoses Acute Eosinophilic ... Constitutional Symptoms
Causes of Eosinophilia - Differential Diagnosis
Bugs:
 - Fungus (aspergillosis)
 - Viral (HIV)
 - Ectoparasites (scabies, myiasis)
Causes of Eosinophilia ... DRESS - AIN - Eosinophilic ... Asthma Tugs (vasculitis ... coyefish379 #Eosinophilia ... Differential #Diagnosis #Causes
Infectious causes of eosinophilia

By Dr. Hawra Al-Lawati @hawraallawati via Febrile [febrilepodcast.com]
#ID  #Infectious Diseases  #Infections
#Differential
Infectious causes ... of eosinophilia ... Ddx #Diagnosis #eosinophilia ... #eosinophil #fever