11 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
RPGN has three primary ... pathophysiologic causes ... Purpura Anti-GBM antibodies ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
) • Systemic lupus ... drug-induced SLE) • Systemic ... Anti-U1-RNP ANCA-Associated ... Vasculitis: • ... #diagnosis #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: ANCA Associated ... tract, and often causes ... • Drug Associated ... C-ANCA) pattern: antibodies ... differential #diagnosis #rheumatology
Causes of Petechial Rash - Differential Diagnosis Algorithm

Pinpoint areas (less than 2 mm) of hemorrhage, which
Causes of Petechial ... Differential Diagnosis Algorithm ... Abnormalities in primary ... Infection - Vasculitis ... #Causes #dermatology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
form: not associated ... Hypocomplementemia • Can cause ... ) • Cutaneous vasculitis ... Nephrogenic DI Hematologic ... Vasculitis: •
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
with GCA or as primary ... Rash, arthritis Primary ... : ANCA Associated ... tract, and often causes ... Differential #Diagnosis #Rheumatology
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
SLE (Systemic Lupus ... Diagnosis: • ANCA-associated ... the context of primary ... 1, SCL-70, RNP antibodies ... Malignancy Associated
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Primary (essential ... malignancies, vasculitis ... processes: • Systemic ... cryoglobulins • Negative causes ... #hematology
PALM RASHES 
Common features and patterns:
1.	Color:
o	Red or erythematous: Common in inflammatory or allergic reactions.
o	Purple or purpuric:
suggest vascular or hematologic ... inflammation (vasculitis ... 2 Texture: o Flat ... Rash appears as flat ... infections. 5 Associated
Polymyalgia Rheumatica (PMR) Diagnosis and Management Summary

WHAT?
 • Polymyalgia rheumatica (PMR) is a common systemic inflammatory
PMR) is a common systemic ... disease of unknown cause ... • Associated ... DIAGNOSIS: • PMR primarily ... anti-citrullinated peptide antibodies