20 results
Diagnostic algorithm for a child or adolescent with suspected pulmonary hypertension. CHD, congenital heart disease; CPET,
testing; CTEPH, chronic ... dysplasia; CLD, chronic ... lung disease; LFT ... , liver function ... #Diagnosis #Peds
Causes of Pulmonary Hypertension - Differential Diagnosis Algorithm
Pulmonary Arterial Hypertension
 • Idiopathic
 • Associated with:
Causes of Pulmonary ... Differential Diagnosis ... Algorithm Pulmonary ... • Valvular Lung ... Metabolic Disorders Chronic
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
• Irregular Etiology ... • Secondary to ... chronic lung disease ... • Hypoxia • Pulmonary ... hypertension
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Pulmonary hypertension ... due to lung disease ... Interstitial lung ... Classification #Diagnosis #Differential ... #Causes
Right-Sided Heart Failure - Differential Diagnosis Algorithm
Cardiac Causes - Rule out Left-Sided Heart Failure (Most Common):
Heart Failure - Differential ... • Chronic ... • Diffuse Lung ... Lung Infection ... Arterial Hypertension
Causes of Dyspnea - Differential Diagnosis Algorithm
Cardiac:
 • Dysrhythmia
 • Ischemia
 • Cardiomyopathy
 • Valvular disease
Causes of Dyspnea ... - Differential ... Bronchitis • Chronic ... • Interstitial lung ... hypertension
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
ILD caused by inhalation ... Methotrexate ILD Secondary ... pneumonia: Acute, Chronic ... ILD #diagnosis #differential ... #pulmonary #causes
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Causes of Interstitial ... Differential Diagnosis ... Impaired cardiac function ... Beomycin • Acute or Chronic ... #Differential #
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
inflammation causes ... Most Common Causes ... hypertension • ... function tests: ... #differential #
Portopulmonary Hypertension
Presence of pulmonary arterial hypertension in a patient with portal hypertension
No other obvious causes (chronic
Presence of pulmonary ... other obvious causes ... (chronic lung disease ... RVSP) - Estimates pulmonary ... - Mechanism: causes