19 results
Krabbe Disease 

Check out this interesting case of Krabbe disease, a rare genetic leukodystrophy. Diagnosis was
Diagnosis was made ... testing and expedite treatment ... leukodystrophy w/ deficiency ... • Dec NAA, inc Cho ... #MRI #Clinical
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
, motile, beta-hemolytic ... food, salad bar Clinical ... Invasive disease) • CSF ... Infection) • MRI ... infectiousdiseases #treatment
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
, motile, beta-hemolytic ... food, salad bar Clinical ... Invasive disease) • CSF ... Infection) • MRI ... infectiousdiseases #treatment
Blood Product Transfusions One Pager Summary
Type and screen - determines blood type and detects in recipient
• Washed RBC ... recipients w/ IgA deficiency ... patients with CHF ... #Transfusions #diagnosis ... #management #hematology
Differentiation Syndrome in APML
Epidemiology:
 • Incidence: common in APL (2-48% depending on the study)
 • Triggers:
Triggers: ATRA treatment ... sepsis), PE, DAH, CHF ... Renal Failure Treatment ... #management #hematology ... #oncology
Aplastic Anemia - Overview

Who?
• M = F
• 3 peaks:	1) Childhood	2) 15-25 years	3) >60 years

What?
• Aplastic anemia
Aplastic Anemia Clinical ... Pancytopenia: • ↓ RBC ... aplastic anemia Treatment ... Aplastic #Anemia #oncology ... #hematology #diagnosis
Refeeding Syndrome Overview

What Is It?
	• Electrolyte/fluid shifts caused by initiation of nutrition in severely malnourished patient.
may cause severe clinical ... decompensation (CHF ... • Seizures • Hemolysis ... hyperparathyroidism Treatment ... #Differential #Diagnosis
Blood Transfusion Reactions

Immune Mediated:
 • Febrile Non-Hemolytic Transfusion Reaction (FNHTR): Most common immune reaction to transfusion.
recipients w/ IgA deficiency ... patients with CHF ... Hyperkalemia: Citrate in RBCs ... RBCs (stored at ... #Transfusion #diagnosis
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Clinical ... Guillain-Barre Diagnosis ... WBC (Albuminocytologic ... axonal form • MRI ... #management #treatment
Chronic Lymphocytic Leukemia (CLL) - Summary
Overview: 
 • Most common leukemia in adults
 • Disorder of
minimal tumor burden Diagnosis ... immunophenotype Clinical ... Lymphocytic #Leukemia #oncology ... #hematology #hemeonc ... #diagnosis #management