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Hypereosinophilia and Hypereosinophilic Syndrome

 • Secondary Hypereosinophilic Syndrome
 • Clinically Relevant HES Variants
 • When to
Hypereosinophilia ... and Hypereosinophilic ... Diagnosis and Treatment ... HES #Hematology #eosinophilia ... #eosinophils #diagnosis
Differential Diagnosis of Pulmonary Eosinophilia
Infection:
 • Helminthic: Loffler syndrome (Ascaris, hookworm, Strongyloides), Tropical pulmonary eosinophilia (lymphatic
Differential Diagnosis of Pulmonary ... Strongyloides), Tropical pulmonary ... Acute chronic pulmonary ... eosinophilia, Hypereosinophilic ... #Pulmonary #Differential
Eosinophil Disorders Testing Algorithm
INDICATIONS FOR TESTING:
 • Peripheral blood eosinophilia/hypereosinophilia uncovered incidentally during medical evaluation or
Eosinophil Disorders ... Peripheral blood eosinophilia ... /hypereosinophilia ... 1,500 cells/µL • Hypereosinophilia ... glucocorticoid treatment
Eosinophilia - Differential Diagnosis Algorithm
Idiopathic Eosinophilia
Primary Eosinophilia:
 • Primary hypereosinophilic syndrome
 • Eosinophilic Leukemia
 • MPN/MDS
Eosinophilia - Differential ... Primary Eosinophilia ... : • Primary hypereosinophilic ... syndrome • Eosinophilic ... Secondary Eosinophilia
Eosinophilic Pneumonia
When to suspect Eosinophilic Pneumonia? Non-resolving pneumonia + BAL > 25% eosinophils + excluded more
Eosinophilic Pneumonia ... When to suspect Eosinophilic ... diagnoses Acute Eosinophilic ... Consolidations AKA "inverse pulmonary ... Pneumonia #diagnosis #pulmonary
Causes of Eosinophilia - Differential Diagnosis
Bugs:
 - Fungus (aspergillosis)
 - Viral (HIV)
 - Ectoparasites (scabies, myiasis)
Causes of Eosinophilia ... DRESS - AIN - Eosinophilic ... Leukemia - Primary Hypereosinophilic ... Syndrome - Chronic Eosinophilic ... coyefish379 #Eosinophilia
Approach to Eosinophilic Lung Diseases
 • Acute Eosinophilic Pneumonia (< 1 wk) - ~30yo, M; Recent
Approach to Eosinophilic ... Diseases • Acute Eosinophilic ... SOB • Chronic Eosinophilic ... , CV, renal • Hypereosinophilic ... Lung #Diseases #pulmonary
Hypereosinophilia Syndrome (HES) - Diagnosis and Management
Definition: An absolute eosinophil count (AEC) greater than 1500 and
Hypereosinophilia ... attributable to eosinophilia ... confirmed tissue eosinophilia ... with blood eosinophilia ... Alert_Oriented3 #Hypereosinophilia
On the left a case of chronic eosinophilic pneumonia.
It was a patient with low-grade fever, progressive
case of chronic eosinophilic ... There was a marked eosinophilia ... Chronic eosinophilic ... Chronic eosinophilic ... respond promptly to treatment
Hypereosinophilia (HE) Summary

 • Definition
 • When to Suspect?
 • A Partial Classification of Hypereosinophilia
 •
Hypereosinophilia ... Classification of Hypereosinophilia ... Presentations • Treatment ... @ZhuoerXie #Hypereosinophilia