13 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
skin injury) • Neurologic ... basal ganglia, CNS ... meningitis), MCC CNS ... collaboration • CNS ... • Nonsurgical abdominal
Left Abducens Spasm on Physical Exam

A 50 yr male with left facial spasm and diplopia, with
Abducens #Spasm #CNVI ... #CN6 #PhysicalExam ... #clinical #ocular ... ophthalmology #neurology ... #video
Neuromyelitis Optica (NMO) - Clinical Manifestations
 • Optic neuritis: Reduced visual acuity, ranging from mild to
desaturation, Scotoma, Ocular ... (AQP4-lgG disease ... pain • Extra-CNS ... Manifestations #diagnosis ... #neurology #symptoms
Distal Renal Tubular Acidosis
Distal RTA is the true Nephrogenic RTA and can be truly divided into
A intercalated cells ... - Autoimmune diseases ... (Sjogren's Syndrome ... mutations) - CNI ... Acidosis #RTA #diagnosis
Ptosis - Differential Diagnosis Framework

Ptosis (Greek- to fall) Drooping of the upper eyelid that usually results
- Differential Diagnosis ... CN III palsy 2. ... Neurogenic Ptosis - Neurologic ... disease affecting ... #Ptosis #neurology
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Diagnosis: • Dry ... gland) biopsy • Ocular ... Parotid swelling CNS ... nervous system (CNS ... • 8%-27% for CNS
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
- Differential Diagnosis ... affects the skin, neurologic ... multiplex • GI tract: Abdominal ... gut involvement, abdominal ... chorioretinitis, CNS
Leukemias Overview: ALL, CML, AML, APML, CLL

Acute leukemias > 20% blasts in the peripheral blood smear
extramedullary disease ... involvement • 30%: CNS ... , weight loss, abdominal ... : CNS manifestations ... Hematology #Oncology #Diagnosis
Hypertrophic Pachymeningitis - Differential Diagnosis Framework

Pachymeningitis is a rare condition that causes areas of a layer
- Differential Diagnosis ... Neurosyphilis • CNS ... pachymeningitis • CNS ... brain sagging syndrome ... Pachymeningitis #HP #Neurology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... et diutinum Neurologic ... Scleromyxedema (CNS ... Sneddon-Wilkinson disease ... #Differential #Diagnosis