68 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Manifestations of Granulomatosis ... involvement in granulomatosis ... presentation of the disease ... GPA causes disease ... rash #diagnosis #rheumatology
2021 ACR/VF Guidelines for Management of Eosinophilic Granulomatosis with Polyangiitis (EGPA)

#EGPA #Eosinophilic #Granulomatosis #Polyangiitis #ACR2021 #Management
Guidelines for Management ... of Eosinophilic Granulomatosis ... #Eosinophilic #Granulomatosis ... Polyangiitis #ACR2021 #Management ... #rheumatology #
2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Guidelines for Management ... of Granulomatosis ... Polyangiitis (MPA) #Granulomatosis ... #MPA #ACR2021 #Management ... #rheumatology #
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... for Treatment & Management ... Nodosa (PAN) • Granulomatosis ... • Eosinophilic Granulomatosis ... Guidelines #algorithm #rheumatology
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
connective tissue disease ... ANCA+ 90% • Granulomatosis ... 90% • Anti-GBM disease ... antibodies #diagnosis #rheumatology ... #diseases
Proposed Treatment Algorithm for MAS / HLH

#MAS #HLH #Hemophagocytic #Lymphohistiocytosis #Management #Treatment #Algorithm #Hematology
Hemophagocytic #Lymphohistiocytosis ... #Management #Treatment ... #Algorithm #Hematology
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
Malabsorption • Granulomatous ... breast cancer Granulomatous ... and M panel Management ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
- Kawasaki disease ... - Wegener granulomatosis ... and infectious diseases ... - serum disease ... Vessels #Diagnosis #Rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Hemophagocytic Lymphohistiocytosis ... • Autoimmune diseases ... Adult-onset Still disease ... #diagnosis #management ... treatment #summary #rheumatology
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
Autoantibodies and their Disease ... Wegener's granulomatosis ... (TTG) - Celiac disease ... #Associations #diseases ... diagnosis #table #rheumatology