12 results
Summary of Coagulation Deficiencies
Inherited:
 • Hemophilia A - Deficiency of Factor VIII
 • Hemophilia B -
Hemophilia A - Deficiency ... celiac disease, CF, IBD ... Deficiencies #Summary #table ... comparison #diagnosis #hematology ... #deficiency
Management of Lupus Nephritis
Lupus nephritis (LN) in 10 to 40% of SLE
Hallmark = proteinuria 20.5 g/g
Management of Lupus ... Lupus #Nephritis #Management ... #treatment #management ... #rheumatology # ... nephrology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
cytokines (TNFa,lL1, IL6 ... Cellular immune deficiency ... Lymphohistiocytosis #diagnosis #management ... treatment #summary #rheumatology
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
Prognosis: Usually mild ... Usual therapeutic management ... sle #comparison #table ... #rheumatology # ... diagnosis #management
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Non-autoimmune rheumatologic ... disease • Prolidase deficiency ... • Acute lupus pneumonitis ... CNS • Headache, mild ... Erythematosus #Diagnosis #Rheumatology
Hemophilia A Prophylaxis (Factor Eight Deficiency)

Who Needs Prophylaxis?

Primary Prophylaxis:
 • Severe deficiency (activity level <1%) even
(Factor Eight Deficiency ... Prophylaxis: • Severe deficiency ... bleeding episodes • Mild-to-moderate ... #FactorEight #Deficiency ... #hematology #management
Algorithm for managing FVII deficiency.

*Mild bleeding history includes minor epistaxis, menorrhagia, gastrointestinal bleeding, joint and soft
managing FVII deficiency ... *Mild bleeding history ... #FVII #deficiency ... Factor7 #Algorithm #management ... #Hematology
Renal Replacement Therapy (RRT) - ICU One Pager Summary
Indications (AIEOU):
 • A: Acidosis (usually severe metabolic)
in the ICU: • IHD ... (Sustained low efficiency ... #Therapy #RRT #managment ... #nephrology #CRRT
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
- Pleocytosis: Mild ... • Nutritional Deficiency ... Myelitis #diagnosis #management ... #neurology #differential
Management of Pruritus in Patients with Chronic Kidney Disease
Pruritus with no primary lesions - differential diagnosis:
Management of Pruritus ... pruritus (Iron deficiency ... Polycythemia vera) Management ... Use mild detergent ... #Nephrology #CKD