39 results
Ophthalmoplegia secondary to Orbital Apex Syndrome

A 61-year-old man presented with retro-orbital pain, near-complete ophthalmoplegia, loss of
to Orbital Apex Syndrome ... A 61-year-old ... Orbital #Apex #Syndrome ... #Clinical #Video ... #PhysicalExam #NEJM
Pulsatile AAA on Abdominal Exam

A 66-year-old man presented with a 2-month history of abdominal bloating and
Abdominal Exam A 66-year-old ... Aortic #Aorta #Clinical ... #Video #NJEM #vascular
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... not related to clinical ... Hyperviscosity syndrome ... and Ill) • Vascular ... #Rheumatology #
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Clinical Syndrome ... : • Common Clinical ... Features: alveolitis, ear ... myeloid cells NEJM ... Autoinflammatory #Somatic #rheumatology
Jaw Clonus on Physical Exam

A 24-year-old man presented with progressive dysphagia, dysarthria, and weakness in his
Physical Exam A 24-year-old ... consistent with a diagnosis ... #PhysicalExam #Clinical ... #Video #ALS #Neurology ... #NEJM
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
- Diagnosis Diagnostic ... test Most Common Clinical ... medium-large joints) • Vascular ... and peripheral vascular ... #criteria #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... and diplopia) • Vascular ... (Clinical Dx). ... Giant retinal tears ... signs #symptoms #rheumatology
Susac Syndrome - Clinical Triad
 - Central nervous system dysfunction
 - Branch retinal artery occlusion
 -
Susac Syndrome - ... Clinical Triad ... disease flares - 2-year ... SusacSyndrome #Triad #Diagnosis ... #Management #Rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Hyperviscosity, - Vascular ... Cryofibrinogenemia Clinical ... : • + Clinical ... Antiphospholipid syndrome ... #rheumatology #
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Vascular Sludging ... : • Clinical triad ... Labs/Diagnosis: ... Cryoglobulins #diagnosis ... classification #rheumatology