Bile Duct Paucity - Differential Diagnosis
 • Genetic: Alagille syndrome, Trisomy 21, Williams syndrome, Peroxisomal disorders
 • Metabolic: α1-antitrypsin deficiency, Cystic fibrosis, Panhypopituitarism
 • Infections: Congenital cytomegalovirus, Congenital rubella, Congenital syphilis
 • Immune / Inflammatory disorders: Hemophagocytic lymphohistiocytosis, Sclerosing cholangitis, Graft-versus-host disease, Chronic allograft rejection
 • Other: Drug-associated vanishing bile duct syndrome, Biliary atresia (late finding)

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