89 results
Bile Duct Paucity - Differential Diagnosis
 • Genetic: Alagille syndrome, Trisomy 21, Williams syndrome, Peroxisomal disorders
Bile Duct Paucity ... #Bile #Duct #Paucity
Snellen Chart for Mobile - Should be held at arm's length -  Note this has
Mobile #Visual #Acuity
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
90%) P - Post/pauci
Immune Reconstitution Inflammatory Syndrome (IRIS) - Pathophysiology
Risk factors:
 - Low CD4 count
 - Disseminated OI
 -
Disseminated OI - Paucity
Paucis Verbis card: Early goal directed therapy
April 16th, 2010 | ALiEM Cards, Infectious Disease 
By: Michelle
Paucis Verbis card
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Goodpasture's) Pauci-immune
Rapidly Progressive Glomerulonephritis (RPGN) 
 - Loss of kidney function over a short period of tirne
EM deposits Pauci-lmmune
Causes of Acute Kidney Injury (AKI) - Differential Diagnosis Algorithm
Acute Kidney Injury (AKI) - Acute increase
post-strep, lupus) • Pauci-immune
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
ANCA Associated / Pauci ... palpable purpura • Pauci ... • Necrotizing, pauci-immune ... cavities, hemoptysis, pauci-immune
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Syndromes: • Pauci-Immune