Mithu Maheswaranathan, MD @MithuRheum
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Rheumatologist at Duke University Creator of Rheum OnePagers ➡ RheumOnePagers.com Twitter: @MithuRheum ➡ https://twitter.com/MithuRheum
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Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
: • Vasculitides ... : Giant Cell Arteritis ... GCA), Takayasu's arteritis ... Nodosa (PAN), ANCA ... associated vasculitis
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... • Giant Cell Arteritis ... • Takayasu's arteritis ... @MithuRheum #Vasculitis ... ACR2021 #Guidelines #algorithm
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
: The ANA patterns ... Patterns and Associated ... Juvenile Idiopathic Arthritis ... scleroderma), Rheumatoid Arthritis ... Juvenile Idiopathic Arthritis
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Giant Cell Arteritis ... (GCA) - Vasculitis ... Management Algorithm ... #GCA #Vasculitis ... ACR2021 #Guidelines #algorithm
ANA Patterns and Associated Rheumatic Diseases:
 • Homogeneous: Systemic lupus erythematosus (SLE), Mixed connective tissue disease
ANA Patterns and ... Juvenile Idiopathic Arthritis ... Ann Marie Kumfer ... Antinuclear #Antibodies #ANA ... #patterns #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA) and ... Vasculitis Management ... Algorithm - ACR ... #Vasculitis #Management ... ACR2021 #Guidelines #algorithm
Polyarteritis Nodosa (PAN) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Severe Disease → Remission
Nodosa (PAN) - Vasculitis ... Management Algorithm ... MTX or AZA) with ... Polyarteritis #Nodosa #Vasculitis ... ACR2021 #Guidelines #algorithm
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Vasculitis Management ... Algorithm - ACR ... GC + MTX, GC + AZA ... #Vasculitis #Management ... ACR2021 #Guidelines #algorithm
Takayasu's Arteritis (TAK) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active TAK not on
Takayasu's Arteritis ... (TAK) - Vasculitis ... Management Algorithm ... immunosuppressive Rx: MTX, AZA ... #Vasculitis #Management
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
alveolitis, ear and ... recurrent fevers, vasculitis ... syndrome (MDS) and ... • giant cell arteritis