Mithu Maheswaranathan, MD @MithuRheum
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Rheumatologist at Duke University Creator of Rheum OnePagers ➡ RheumOnePagers.com Twitter: @MithuRheum ➡ https://twitter.com/MithuRheum
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Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Cell Arteritis (GCA ... arteritis (TAK) • Polyarteritis ... Polyangiitis (GPA ... Sources: GCA ... ACR2021 #Guidelines #algorithm
Polyarteritis Nodosa (PAN) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Severe Disease → Remission
Polyarteritis Nodosa ... Vasculitis Management Algorithm ... with CYC over GC ... MithuRheum #PAN #Polyarteritis ... ACR2021 #Guidelines #algorithm
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, E1 ... Syndrome (32%) • polyarteritis ... • UBA1 = major E1 ... Syndrome #Vacuoles #E1
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Cell Arteritis (GCA ... Vasculitis Management Algorithm ... with MTX or GC ... GiantCell #Arteritis #GCA ... ACR2021 #Guidelines #algorithm
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA ... Vasculitis Management Algorithm ... , GC+CYC, GC+AZA ... , GC+MMF or GC alone ... ACR2021 #Guidelines #algorithm
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
Cell Arteritis (GCA ... Behcet's Disease, Polyarteritis
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Vasculitis Management Algorithm ... (Can consider GC ... + MEP 2) GC ... + MTX, GC + AZA ... ACR2021 #Guidelines #algorithm
Takayasu's Arteritis (TAK) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active TAK not on
Vasculitis Management Algorithm ... High-dose daily oral GC ... + non-GC immunosuppressive ... ACR2021 #Guidelines #algorithm