10 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Still's Disease Clinical ... Hantavirus • Malignant ... Pulmonary: pleural effusion ... • Ocular: uveitis ... management #treatment #rheumatology
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Clinical suspicion ... Clinical Manifestations ... Persistent pleural effusions ... Testing: • EKG • Echocardiogram ... disproportionate atrial
Amyloidosis on POCUS Echocardiogram - Subcostal 4 Chamber (S4C)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... large pericardial effusion ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Apical 4 Chamber (A4C)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... large pericardial effusion ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Parasternal short axis (PSAX)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... large pericardial effusion ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Parasternal long axis (PLAX)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... large pericardial effusion ... Cardiac #POCUS #clinical ... #Echocardiogram
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Disorders: • Malignancy ... Cryofibrinogenemia Clinical ... pulmonary emboli, and ocular ... Diagnosis: • + Clinical ... Cryofibrinogenemia #diagnosis #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Rheumatic pain Clinical ... , parts of the axial ... Diagnosis: • A clinical ... as infectious, malignant ... SAPHO #Syndrome #Rheumatology
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... Erythematous, macular ... Non-autoimmune rheumatologic ... Infections • Malignancy ... Lungs: • Pleural effusions
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
gland) biopsy • Ocular ... salivary ducts Clinical ... thickening or effusion ... PE, Pulmonary amyloidosis ... and Arthritis Malignancy