1060 results
Systemic Lupus Erythematosus (SLE) - Diagnosis and Management Summary
 • Epidemiology: 10-180/100,000, Typically Age 20-40, F:M
40, F:M 9:1 • Clinical ... ANA > - Anti-ENA ... to 30% - Anti-dsDNA ... life-threatening • Treatment ... Evolution: Chronic disease
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
to 1:1 F:M • Clinical ... constitutional symptoms • Treatment ... 40, F:M 9:1 • Clinical ... life-threatening • Treatment ... Evolution: Chronic disease
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
accumulation of clinical ... Assessment • Clinical ... • Autoimmune diseases ... Adult-onset Still disease ... Unknown cause Treatment
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis Clinical ... neuropathy Treatment ... - Specific anti-infectious ... the absence of anti-infectious ... with refractory disease
Autoimmune Hepatitis

Clinical Presentation
 - Highly variable clinical presentation, from subclinical disease to acute liver failure.
 -
Autoimmune Hepatitis Clinical ... Highly variable clinical ... from subclinical disease ... & Anti-ALC Abs ... regarding need for treatment
Myasthenia Gravis - Summary
 • an autoimmune disease of the postsynaptic neuromuscular junction associated with antibodies
an autoimmune disease ... Diagnosis: • Based on clinical ... - but 5% have anti—muscle-specific ... treatment Of ocular ... - Improves clinical
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
• Antibodies: Anti-Ro ... /SSA & Anti-La/SSB ... Antibodies: • Anti-Ro ... salivary ducts Clinical ... Adenocarcinoma Treatment
Celiac disease is an immune-mediated, multisystem disorder that affects genetically susceptible individuals who are exposed to
Celiac disease is ... antibodies measured are anti-tissue ... numerically) and anti-endomysial ... test for whom clinical ... is the primary treatment
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
Clinical Manifestations ... poisoning, Parkinson's disease ... Person Syndrome Treatment ... Baclofen • Severe Disease ... Diagnosis #Management #treatment
Staphylococcal Scalded Skin Syndrome (SSSS) 
(aka Ritter disease) 
Nikolsky positive 
Clinical 
• Typically occurs 3 to
(aka Ritter disease ... Nikolsky positive Clinical ... oxacillin (or any anti-staphylococcal ... CA-MRSA or initial treatment