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Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
interstitial lung diseases ... SSc: systemic sclerosis ... arthritis SLE : systemic ... Comparison #Table #Pulmonary ... #Rheumatology #
Systemic Sclerosis Associated Autoantibodies
Anti-topoisomerase I (anti-Sc170): Diffuse skin disease, Pulmonary fibrosis
Anti-centromere: Limited skin disease (~93-95%), Pulmonary
Systemic Sclerosis ... : Diffuse skin disease ... , Pulmonary fibrosis ... (~93-95%), Pulmonary ... Autoantibodies #diagnosis #rheumatology
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
autoimmune disease ... calcinosis • Pulmonary ... interstitial lung disease ... ), PAH (pulmonary ... Scleroderma #SSc #rheumatology
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... solid cancers • Systemic ... hepatitis • Pulmonary ... #diagnosis #management ... #treatment #rheumatology
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
• Homogeneous: Systemic ... ) • Speckled: Systemic ... • Peripheral: Systemic ... , Interstitial Pulmonary ... ANA #patterns #rheumatology
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
Systemic Lupus Erythematosus ... • MCTD (SLE/systemic ... @AnnKumfer #Systemic ... Summary #diagnosis #rheumatology ... #management
Gadolinium Enhancement Patterns in Ischemic and Non-Ischemic Cardiomyopathies
Ischemic:
 • Subendocardial Infarct
 • Transmural Infarct
Non-Ischemic:
 • Mid-wall
e.g.congenital heart disease ... , pulmonary hypertension ... : Amyloidosis, systemic ... cardiomyopathy #diagnosis #cardiology ... #radiology
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
ophtho referral • Systemic ... : • Systemic steroids ... : • Systemic steroids ... Syndrome #Treatment #management ... #pharmacology #rheumatology
Causes of Palpitations
 • ARRHYTHMiA 
 • SINUS ARRYTHMIA 
 • ATRIAL FIBRILLATION 
 • ATRIAL
ACQUIRED VALVULAR DISEASE ... DRUG WITHDRAWAL SYSTEMIC ... PHAEOCHROMOCYTOMA • PULMONARY ... DISEASE • HYPOXIA ... Differential #Diagnosis #Cardiology
Multifocal Atrial Tachycardia (MAT)
• At least 3 different P wave morphologies: 
• Rate 100-180
• Irregular 
Etiology
to chronic lung disease ... • Hypoxia • Pulmonary ... hypertension Management ... Tachycardia #MAT #Cardiology ... Diagnosis #ECG #EKG #Management