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Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
Non-HCV infectious mixed ... Diagnosis, causes and management ... with refractory disease ... #Rheumatology # ... #Diagnosis #Management
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... - Kawasaki disease ... scleroderma - mixed ... Vessels #Diagnosis #Rheumatology
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
- French Vasculitis ... lenalinomide MIXED ... /or refractory disease ... #Management #Rheumatology ... #Monoclonal #Mixed
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
Autoantibodies and their Disease ... c-ANCA - Vasculitis ... granulomatosis p-ANCA - Vasculitis ... RNP antibody - Mixed ... diagnosis #table #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... arthritis, obstructive pulmonary ... Complement (Low levels mixed ... differential #diagnosis #rheumatology
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
interstitial lung diseases ... MCTD : mixed connective ... tissue disease. ... Comparison #Table #Pulmonary ... #Rheumatology #
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
due to lung disease ... pulmonary disease ... with mixed restrictive ... neurofibromatosis, vasculitis ... , Gaucher disease
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Rheumatoid arthritis, Mixed ... • Idiopathic pulmonary ... Sarcoidosis • Vasculitis ... Acute, Chronic • Pulmonary ... #differential #pulmonary
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
seen with the mixed ... Etiology - Mixed ... • Autoimmune diseases ... II and III are Mixed ... classification #rheumatology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- Bone marrow disease ... deficiency • Liver disease ... Von Willebrand disease ... Cryoglobulinemia (MIXED ... #rheumatology #