12 results
ANCA Vasculitis - GPA, MPA, Eosinophilic GPA

doi:10.1038/s41572-020-0204-y

#ANCA #Vasculitis #GPA #MPA #Eosinophilic #rheumatology #diagnosis #comparison #table
ANCA Vasculitis ... - GPA, MPA, Eosinophilic ... #Vasculitis #GPA ... #MPA #Eosinophilic ... diagnosis #comparison #table
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
polyangiitis (GPA ... polyangiitis (MPA ... polyangiitis (EGPA ... vasculitis - MPO ... #Rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
(C-ANCA): GPA > ... >> MPA > eGPA • ... MPO-ANCA (P-ANCA ... ): eGPA, MPA >>> ... Glomerulonephritis #Vasculitis
Frequency of ANCA Positivity in Different Conditions
ANCA-Associated Vasculitis
 • GPA - PR3-ANCA 75%, MPO-ANCA 20%, 5%
GPA - PR3-ANCA 75% ... , MPO-ANCA 20%, ... • MPA - PR3-ANCA ... ANCA 5%, MPO-ANCA ... PR3 #diagnosis #rheumatology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Guidelines for Treatment ... Polyangiitis (GPA ... Polyangiitis (MPA ... #Management #Treatment
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (MPA ... ) - ANCA Vasculitis ... #Polyangiitis #MPA ... #ANCA #Vasculitis ... #Management #Treatment
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
myeloperoxidase (MPO-ANCA ... Associated (Commonly MPO-ANCA ... 100 % Commonly MPO-ANCA ... Vasculitis: + MPO-ANCA ... differential #diagnosis #rheumatology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Cryoglobulinemia (MIXED) • ANCA ... - GPA - EGPA ... - MPA • CTD ... Differential #Diagnosis #hematology ... #rheumatology #
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
) - ANCA Vasculitis ... #Polyangiitis #ANCA ... #Vasculitis #Management ... #Treatment #ACR2021 ... Guidelines #algorithm #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
myeloperoxidase (MPO-ANCA ... present in > 30 / MPO ... > PR3 60/ GPA ... + MPO) Cryoglobulinemic ... Differential #Diagnosis #Rheumatology