118 results
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
central nervous system ... (CNS) involvement ... important, as early diagnosis ... • Systemic lupus ... #differential #diagnosis
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation Syndrome ... Periodic fever syndromes ... (CNS) dysfunction ... #Diagnosis #Management ... #Hematology #Rheumatology
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
of Systemic Lupus ... Demyelinating Syndrome ... permeability Diagnosis ... #neurology #rheumatology ... #management #treatment
ANA Patterns and Associated Rheumatic Diseases:
 • Homogeneous: Systemic lupus erythematosus (SLE), Mixed connective tissue disease
• Homogeneous: Systemic ... ) • Speckled: Systemic ... SLE), Sjogren's Syndrome ... ANA #patterns #rheumatology ... #diagnosis #differential
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
block • Sjogren syndrome ... polymyositis overlap syndrome ... #SLE #Summary #diagnosis ... #rheumatology # ... management
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
central nervous system ... disease - systemic ... Vasculitis #Vessels #Diagnosis ... #Rheumatology # ... Diagnosis
Top tips for triaging and treating kids with Pitt Hopkins Syndrome
#Diagnosis #Management #PatientInfo #Peds #Pediatrics #PittHopkins
with Pitt Hopkins Syndrome ... #Diagnosis #Management ... PatientInfo #Peds #Pediatrics ... #PittHopkins #Syndrome
Raynaud Phenomenon Differential Diagnosis:

Rheumatologic

 - MCC systemic sclerosis, RA, SLE, Sjogren syndrome, Antisynthetase syndrome, MCTD
Heme

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Phenomenon Differential Diagnosis ... : Rheumatologic ... - MCC systemic ... , SLE, Sjogren syndrome ... - Frostbite #Diagnosis
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome) 
An rare systemic acute febrile vasculitic syndrome. Aetiology unknown. 
Affects
Mucocutaneous Lymph Node Syndrome ... ) An rare systemic ... febrile vasculitic syndrome ... Early diagnosis ... #Peds #Pediatrics
Connective tissue disease-associated interstitial lung diseases

LIP: lymphoid interstitial pneumonia. NSIP: nonspecific interstitial pneumonia. OP: organizing pneumonia.
SSc: systemic sclerosis ... PSS: Sjogren syndrome ... arthritis SLE : systemic ... LungDisease #CTILD #Diagnosis ... Table #Pulmonary #Rheumatology