41 results
Krabbe Disease 

Check out this interesting case of Krabbe disease, a rare genetic leukodystrophy. Diagnosis was
Diagnosis was made ... testing and expedite treatment ... neurotoxic • Symptoms ... • Dec NAA, inc Cho ... #MRI #Clinical
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
food, salad bar Clinical ... Invasive disease) • CSF ... Infection) • MRI ... / CT if focal symptoms ... infectiousdiseases #treatment
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
food, salad bar Clinical ... Invasive disease) • CSF ... Infection) • MRI ... / CT if focal symptoms ... infectiousdiseases #treatment
Posterior Ankle Impingement (Os Trigonum) Syndrome - MSK Radiology
Imaging Findings:
 • Os trigonum which has marrow
(Os Trigonum) Syndrome ... flexion but no symptoms ... #clinical #mri ... #clinical #Radiology ... #diagnosis #msk
Optic Neuritis - Diagnosis and Management
 • Epidemiology: Female (75%), 18-50 years,
caucasian
 • Symptoms: Moderate visual
Optic Neuritis - Diagnosis ... caucasian • Symptoms ... R-G or B-Y • MRI ... lesions (b) • CSF ... #rheumatology #
BEE Syndromes - Non-inflammatory Causes

Immune-mediated conditions affecting the Brain, Eye, and Ear

Visual or auditory symptoms in
Visual or auditory symptoms ... conjunction with symptoms ... and treatment can ... neuropathy (LHON) plus MRI ... lesions and clinical
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
Guillain-Barre Clinical ... Guillain-Barre Diagnosis ... axonal form • MRI ... #diagnosis #management ... #treatment #neurology
Restrictive Cardiomyopathy - Diagnosis and Causes
Clinical: Dyspnea, Exercise Intolerance, ↑ "Right Sided-Symptoms" (ascites, hepatomegaly, ↑↑peripheral edema)
Physical
and Causes Clinical ... ↑ "Right Sided-Symptoms ... Echocardiography, Cardiac MRI ... Hyper-eosinophilc Syndrome ... #differential #cardiology
Differentiation Syndrome in APML
Epidemiology:
 • Incidence: common in APL (2-48% depending on the study)
 • Triggers:
Differentiation Syndrome ... Triggers: ATRA treatment ... : >3 symptoms, or ... sepsis), PE, DAH, CHF ... Renal Failure Treatment
Posterior Reversible Encephalopathy Syndrome (PRES) Overview

Clinico-Radiological Syndrome, characterized by:
 • Headache
 • Seizures
 • Altered mental
brain PRES Clinical ... Neurological symptoms ... Vascular narrowing on MRA ... epilepticus Treatment ... underlying cause • Treatment