241 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
staining): • Low Complement ... Idiopathic • Normal Complement ... With associated pulmonary ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... ANCA Associated Vasculitis ... anti-GBM) 10%: - Low Complement ... - Normal Complement ... Kumfer @AnnKumfer #Pulmonary
A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... #Differential #Algorithm
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... destructive sinusitis, pulmonary ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis ... #vasculitis #differential
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Hypocomplementemic Urticarial Vasculitis ... Complex Formation - Complement ... Formation -> Vasculitis ... Hypocomplementemic #Urticarial #Vasculitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... arthritis, obstructive pulmonary ... against MPO • Complement
Petechiae/Purpura - Diagnostic Algorithm. Pathophysiology: 1) Represent the passage of erythrocytes from the intravascular to extravascular
Purpura - Diagnostic Algorithm ... trauma, infection, vasculitis ... process such as vasculiitis ... commonly renal and pulmonary ... Purpura #Palpable #Algorithm
Hemoptysis Differential Diagnosis Framework
Cardiovascular: Pulmonary embolism, Heart failure, Vasculitis, Valvular disease, Arteriovenous malformation
Pulmonary - Airway: Bronchitis,
Cardiovascular: Pulmonary ... Heart failure, Vasculitis ... Arteriovenous malformation Pulmonary ... Differential #Diagnosis #algorithm ... #pulmonary
Causes of Hemoptysis - Differential Diagnosis Algorithm
Massive Hemoptysis (>I00 mL in 24 hours)
 • Malignancy
 •
Differential Diagnosis Algorithm ... Vasculitis Infection ... Vasculitis • ... Differential #Diagnosis #Algorithm ... #Causes #Pulmonary
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... , small-vessel vasculitis ... Complement levels ... Levamisole-induced vasculitis ... ANCA #Associated #Vasculitis