23 results
Krabbe Disease 

Check out this interesting case of Krabbe disease, a rare genetic leukodystrophy. Diagnosis was
Diagnosis was made ... testing and expedite treatment ... with clinical trials ... • Symmetric abnormal ... #MRI #Clinical
Myocarditis
Diagnosis 
• Endomyocardial biopsy (gold standard, rarely performed) 
• Clinical presentation 
• Cardiovascular MRI 
Clinical 
•
Myocarditis Diagnosis ... Cardiovascular MRI ... summation gallop • Abnormal ... shock, sudden cardiac ... #Myocarditis #Diagnosis
Cardiac Amyloid - Diagnosis, Signs, Symptoms and Management

Clinical Presentation
- exertional dyspnea
- peripheral edema
- exertional syncope
- peripheral
Cardiac Amyloid ... - Diagnosis, Signs ... Management Clinical ... precordial leads) - atrial ... #Diagnosis #Stages
Wolff-Parkinson-White Syndrome

WPW is a congenital abnormality characterized by an abnormal accessory conduction pathway between the atria
characterized by an abnormal ... pathway between the atria ... The definitive treatment ... Electrocardiogram #Clinical ... #Diagnosis
Hydroxyapatite Deposition Disease (HADD) - MSK Radiology
Imaging Findings:
 • Ovoid hypointense structures along the bursal surface
Disease (HADD) - MSK Radiology ... • MRI shows globular ... • Treatment for ... #mri #clinical ... #Radiology #diagnosis
Myocarditis 

5 Principles of
Myocarditis:
1. Build clinical suspicion
2. Decide on EMBx
3. Manage acute cardiac injury
4. Manage chronic
Build clinical suspicion ... Manage acute cardiac ... Low voltage Treatment ... agent, steroids, AC ... #Myocarditis #diagnosis
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Still's Disease Clinical ... Differential Diaqnoses ... , DIC, TMA • Cardiac ... Stills #Disease #diagnosis ... #management #treatment
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
shunt (Type 2) Clinical ... left heart 3-6 cardiac ... cycles after right atrial ... blood gas (ABC) ... #management #treatment
Haglund Syndrome - MSK Radiology
Imaging Findings:
 • The Haglund Deformity (enlarged superior margin calcaneal posterior process)
Syndrome - MSK Radiology ... bursa is commonly abnormal ... Differential diagnosis ... #mri #clinical ... #Radiology #diagnosis
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
Differential Diagnosis ... ancestry, LGE on MRI ... and timing with Cardio-OB ... follow-up with Cardio-OB ... #treatment